Extramammary Paget's disease: A case report

Extramammary Paget's disease is a derma­tosis which pathologically and clinically resembles Paget's discase of the breast.

The disease occurs in regions with apo­crine glands; most often in the anogenital area, seldom in the axilla. A few cases of the discase are described in the umbilicus, the mucous membrane of the mouth, in the nose, ear and in the gland of Moll, of the eyelid.

Women get the disease twice as often as men. Most of the patients are older per­sons, the average age being about 60 years. The youngest patient we have found in the literature was a 24-year-old woman with the lesion in the vulva.

Until 10 years ago extramammary Paget's disease was looked upon as a rare entity. During the past few years it has been reported in increasing numbers, including several cases reported by Scandinavian authors.

Since this condition still is of interest due to both clinical and pathological prob­lems the following case is presented.

Case report: A 72-year-old man was admitted to the hospital with a genito-femoral lesion of the skin. The lesion started in the right groin and increased slowly in size for 10 years. It was oozing intermittently. ln the last 1 1/2 years he had observed a papillary growth on the right thigh adjacent to the inguinal fold. There had been considerable pain but no itching. The lesion had been treated for years as "eczema" or mycotic infection with a great number of topical agents.